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KMID : 1130320090520020256
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Korean Journal of Pediatrics
2009 Volume.52 No. 2 p.256 ~ p.260
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A case of idiopathic pulmonary hemosiderosis with seasonal recurrence
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Kwak Ga-Young
Lee Na-Young
Lee Moon-Hee
Lee Soo-Young
Chung Seung-Yun
Kang Jin-Han
Jeong Chang-Mo
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Abstract
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Idiopathic pulmonary hemosiderosis (IPH) is a rare disease affecting mostly children. This disorder is characterized by recurrent episodes of hemoptysis, bilateral diffuse pulmonary infiltrates, and iron-deficiency anemia. An acute fulminant alveolar hemorrhage can be fatal due to respiratory failure, while chronic hemorrhage leads to hemosiderin-laden macrophages and pulmonary fibrosis. Genetic, autoimmune, allergic, environmental, and metabolic mechanisms of pathogenesis have been suggested, but the etiology of IPH remains unknown. We report on a 9-year-old girl with idiopathic pulmonary hemosiderosis who showed seasonal recurrences without cause.
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KEYWORD
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Idiopathic pulmonary hemosiderosis, Seasonal recurrence
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